Amelogenesis Imperfecta is a condition where the enamel does not form correctly during tooth formation. The enamel typically wears faster than normal, and even at an early age. The teeth are highly susceptible for dental caries because the enamel has difficulty protecting the underlying dentin layer. It can occur throughout the mouth or particular teeth that were affected at the same time of amelogenesis (the formation of the enamel.)
This patient had a number of teeth that is affected by a weaker enamel, but teeth were monitored and restored when they became a problem. It can be seen how the enamel wears and exposes the dentin. The second molar was restored with bonded ceramic (Variolink Esthetic, eMax CAD, Ivoclar Vivadent) using the CEREC system (PrimeScan, MCXL, DentsplySirona.) The premolar and the first molar were restored with composite resin (Adhese DBA, Tetric PowerFill composite resin, PowerCure Curing Light, Ivoclar Vivadent.) The post-operative picture was taken immediately after insertion where hypoplastic enamel can appear more opaque when dehydrated. As the teeth hydrate, the blend of the composite resin will be better.